Grown-up Congenital Heart Disease (GUCH): Difference between revisions

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=== Congenitally corrected transposition of the great arteries ===
=== Congenitally corrected transposition of the great arteries ===
=== Introduction ===
=== Introduction ===
[[File:14. ccTGA.PNG|thumb|right|Figure 14. Congenitally corrected transposition of the great arteries. RA, right atrium. LA, left atrium. RV, right ventricle. LV, left ventricle. p, pulmonary artery. ao, aorta. tric, tricuspid valve.]]
[[File:Figure 14. Congenitally corrected transposition of the great arteries.png|thumb|right|Figure 14. Congenitally corrected transposition of the great arteries. RA, right atrium. LA, left atrium. RV, right ventricle. LV, left ventricle. p, pulmonary artery. ao, aorta. tric, tricuspid valve.]]
The congenitally corrected transposition of the great arteries (ccTGA) is characterized by a normal anatomical position of both atria, with an abnormal connection between the atria and the ventricles. The right atrium is connected with the left ventricle and the left atrium is connected with the right ventricle. (Figure 14) Furthermore the aorta arises from the right ventricle and the pulmonary artery from the left ventricle. There are, in conclusion, abnormal atrioventricular connections and abnormal ventricular-arterial connections present in ccTGA.  
The congenitally corrected transposition of the great arteries (ccTGA) is characterized by a normal anatomical position of both atria, with an abnormal connection between the atria and the ventricles. The right atrium is connected with the left ventricle and the left atrium is connected with the right ventricle. (Figure 14) Furthermore the aorta arises from the right ventricle and the pulmonary artery from the left ventricle. There are, in conclusion, abnormal atrioventricular connections and abnormal ventricular-arterial connections present in ccTGA.  
CcTGA is a very rare defect, accounting for about 1% of all congenital heart disease.
CcTGA is a very rare defect, accounting for about 1% of all congenital heart disease.
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=== Introduction ===
=== Introduction ===
[[File:20. Wilhelm Ebstein.jpg|thumb|left|Figure 20. Wilhelm Ebstein (1836 – 1912).]]
[[File:20. Wilhelm Ebstein.jpg|thumb|left|Figure 20. Wilhelm Ebstein (1836 – 1912).]]
[[File:21. Ebstein.PNG|thumb|right|Figure 21. Schematic drawing showing Ebstein’s anomaly of the tricuspid valve. Left: normal heart with openend right ventricle. Right: Ebstein’s anomaly with displacement of the septal and posterior tricuspid leaflet, leading to atrialisation of a significant part of the right ventricle.]]
[[File:Figure 21. Schematic drawing showing Ebstein’s anomaly of the tricuspid valve.png|thumb|right|Figure 21. Schematic drawing showing Ebstein’s anomaly of the tricuspid valve. Left: normal heart with openend right ventricle. Right: Ebstein’s anomaly with displacement of the septal and posterior tricuspid leaflet, leading to atrialisation of a significant part of the right ventricle.]]
Ebsteins anomaly, named after Wilhelm Ebstein (1836 – 1912) (Figure 20) is a congenital heart defect of the morphological tricuspid valve. The prevalence of Ebstein's anomaly is about 1 in 50.000 – 200.000 with a similar incidence in both males and females.
Ebsteins anomaly, named after Wilhelm Ebstein (1836 – 1912) (Figure 20) is a congenital heart defect of the morphological tricuspid valve. The prevalence of Ebstein's anomaly is about 1 in 50.000 – 200.000 with a similar incidence in both males and females.


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