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Normal ECG Short QT ECG Shortened APduration inshort QTsyndrome 40 mV -85 mV
SQT2 (KCNQ1)
/ Ks
/ Ks
Increase
SQT1 (KCNH2)
/ Kr
/ Kr
Increase
SQT3 (KCNJ2)
/ K1
/ K1
Increase
Short QT syndrome mechanism
Normal ECG
Short QT ECG
Shortened APduration inshort QTsyndrome
40 mV
-85 mV
SQT2
(KCNQ1)
/
Ks
/
Ks
Increase
SQT1
(KCNH2)
/
Kr
/
Kr
Increase
SQT3
(KCNJ2)
/
K1
/
K1
Increase
Short QT syndrome mechanism
Courtesy of Louise R.A. Olde Nordkamp, MD, The Netherlands